Numerous congenital anomalies involving the kidney, ureter, and bladder have been described with a duplex collecting system, essentially the duplex ureter, in particular, being the most common anomaly with a reported incidence of 0.8%. There is no harm to the kidney, though some people with duplex kidneys are more prone to urinary infections, reflux and blockages of the urinary tract. Duplicated Collecting System - ScienceDirect VUR is graded according to severity from grade 1 (mild) to grade 5 (severe). The operation was successfully done in a 49-year-old Thai female presented with a full staghorn kidney stone in the lower moiety of the duplex right kidney. Clinical and imaging examinations demonstrated tuberculous contracted bladder with a bilateral duplex collecting system. This occurs due to an incomplete fusion of the upper and lower pole of the kidney which creates two separate drainage systems from the kidney. It is often associated with a division of the kidney into two parts, an upper and lower lobe. Duplication occurs when two separate ureteric buds arise from a single Wolffian duct. Clinically significant duplication of the collecting system may manifest prenatally with upper pole hydronephrosis and dilatation of the upper pole ureter, lower pole hydronephrosis, or a ureterocele within the bladder. Developed by renowned radiologists in each specialty, STATdx provides comprehensive decision support you can rely on - Ureteropelvic Duplications Prenatal imaging features and postnatal outcomes of isolated fetal duplex renal collecting system: A systematic review and meta-analysis Francesca Bascietto, Asma Khalil, Giuseppe Rizzo, Alexander Makatsariya, Danilo Buca, Claudia Silvi, Matteo Ucci, Marco Liberati, Alessandra Familiari, Francesco D'Antonio Duplex collecting systems are seen in 0.7 % of the healthy adult population and 2-4 % of patients investigated for urinary tract symptoms [10]. This chapter will discuss the terminology, incidence, embryology and pathophysiology of duplex kidneys. Meanwhile, renal morphological anomalies in TS include horseshoe kidney, hydronephrosis, duplex collecting system, and single unilateral kidney. Happen with a single ureter or a double ureter (duplex collecting system). However, diagnosis can be made in rare instances during adulthood when duplex collecting systems are usually found incidentally on abdominal imaging or during surgery [ … Single-system ureteroceles are those associated with a single kidney, collecting system, and ureter. Conclusion: A duplex collecting system arises when two ureteral buds are formed during fetal development. Patients usually present in childhood with recurrent UTIs, flank pain, incontinence and hematuria [ 20 ]. The more extensive duplication, however, does often cause problems and can typically mean a child is more prone to urine infections. J Radiol Case Reports. Bilateral Duplex Collecting System with Right Obstructing Stones and Ureterocele - A Case Report with Literature Review ... complications [8]. detected on US, duplex collecting system, preoperative evaluation in PUJO and to look for complications like pyelonephritis, renal stones, and malignancies. Single-system orthotopic ureteroceles appear to respond most definitively with this approach. No treatment is needed. Ureteroceles can be associated with single or duplex collecting systems. We retrospectively reviewed the medical records of patients diagnosed with a duplex system with UPJO. detected on US, duplex collecting system, preoperative evaluation in PUJO and to look for complications like pyelonephritis, renal stones, and malignancies. A duplicated kidney, also referred to as an ureteral duplication or duplicated collecting system, means that a kidney has two ureters draining the kidney rather than the normal one. A 5-year-old girl presented with urinary incontinence regardless of the successful toilet training and a suspicion of left duplex … The patient had a complete duplex collecting system renal function. A duplex collecting system is one of the most common and is caused by a bifurcation of the ureteric bud resulting in two ureters or a Y-shaped ureter. One of the most common CAKUT variations is the duplex kidney, also known as the duplicated ureteral collecting system . The study of Gong, et al. Some of these anomalies are associated with a wide variety of other congenital genitourinary tract abnormalities and have been … However, uretero-inguinal hernias in native kidneys are considered an uncommon finding, especially with a duplex collecting system. However, diagnosis can be made in rare instances during adulthood when duplex collecting systems are usually found incidentally. Prenatal imaging features and postnatal outcomes of isolated fetal duplex renal collecting system: A systematic review and meta-analysis. When … We present the case of a patient who presented with septic complications secondary to this combination. A 27-year-old male patient who underwent renal transplantation in 2017, on 19 April 2018, was presented with a creatinine level of 2.2 mg/dl. Keywords: Cystoscopy • Ureterocele • Complications • Surgery Introduction A ureterocele is basically a cystic dilatation of the distal ureter, a challenging clinical situation because of variance in anatomy and presenting symptoms [1,2]. Duplex collecting systems is the main topic and how it may become complicated by vesicoureteral reflux (VUR) and ureterocele will be covered in this paper. Here, we report a case in which a middle age patient has bilateral duplex urinary collecting systems and horseshoe kidney deformity accompanied with right renal ureteral calculi and hydronephrosis. [ncbi.nlm.nih.gov] A Rare and Unique Case of Bilateral Double Collecting System with Congenital Ureteric Anomalies Presenting as Abdominal Distension in a Two-Year Old Baby Girl. A duplicated ureter is commonly found in … One or both kidneys have two tubes (ureters), not one, draining to the bladder. The duplex collecting system in girls with urinary tract infection: prevalence and significance. A duplex kidney is where a child is born with a double kidney on one side (“duplex” is Latin for “double”). In most cases, an ectopic ureter is associated with a duplex collecting system and complete ureteral duplication. A wide range of structures such as small bowel, large bowel and … In a normal urinary tract, each kidney is connected to one ureter (a tube that drains urine into the bladder). A duplex collecting system can result in frequent urinary tract infections, backflow of urine into the kidney, and sometimes kidney damage. Your browser does not support HTML5 video. Conclusion: Duplex collecting systems are common but clinically insig-nificant. [8]. at 10 mo she had surgery to remove half of her kidney, and then they wanted to see if the duplex collection system would correct itself. Incomplete duplication is most often associated with ureteroureteral reflux or ureteropelvic junction obstruction of the lower pole of the kidney. Most people do not need treatment. In this study, complete duplication showed higher incidence of ectopic ureter and surgical intervention was needed. Causes are unclear but may be genetic. Transl Androl Urol. It can be a complete split from the pyelocalicea to the ureteral orifice in the bladder, also called total duplication or pyelo ureteral duplicity. After birth, urinary tract infections and/or day/nighttime wetting, or flank pain may be presenting signs/symptoms. This is a birth defect and is usually found in childhood. Francesca Bascietto, Francesca Bascietto. A duplex collecting system is one of the most common and is caused by a bifurcation of the ureteric bud resulting in two ureters or a Y-shaped ureter. Ureterocele is rare especially with collecting system duplication in the nonorthotopic (extravesical) position in adult. Non contrast CT can detect renal stones and nephrocalcinosis. The limited duplex kidney (where only the collecting system is double) is usually an incidental finding and rarely causes problems. Somefamilies hadmorethanoneaffected relative. A complete duplex collecting system is usually associated with other congenital anomalies, such as ectopic ureteric insertion, ureterocele, and VUR ( 8 ). How is a duplex kidney treated? A duplex kidney is one kidney that has two separate collecting systems. An adult woman presented with urinary sepsis, and her initial investigation with … Duplex kidneys may be associated with ureterocele, ectopic ureter insertion or vesicoureteric reflux (VUR). 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